Situs Inversus with Levocardia and Congenitally Corrected Transposition of Great Vessels in a 35 year old Male

A Case report

Authors

  • Mohammad Abbasi Teshnizi M.D., Associate Professor, Department of Cardiac Surgery, Faculty of Medicine, Imam Reza Hospital, Mashhad University of Medical Science, Mashhad, Iran

Keywords:

Congenitally Corrected, Levocardia, Situs Inversus

Abstract

Situs inversus with levocardia and congenitally corrected transposition of the great arteries represents a relatively very rare congenital condition and most patients are diagnosed in infancy or early age. This case report describes a 35-year old man with congenitally corrected transposition of the great arteries which presented with a five month history of exertional dyspnea. A diagnosis was confirmed by transesophageal echocardiogram, showing situs inversus, levocardia, atrioventricular and ventriculoarterial discordance. He underwent physiologic repair, and was discharged thirty five days after the operation, in a good general condition. Although management of the corrected transposition of the great arteries patients remains controversial, the recommendation is that physiologic repair may be the procedure of choice for some patients, particularly complicated cases.

 

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Published

2022-01-18